Sarcoma folicular de células dendríticas mediastinal: primer reporte de caso en Costa Rica / Mediastinal Follicular Dendritic Cell Sarcoma: First Case Report in Costa Rica
Respirar (Ciudad Autón. B. Aires)
; 16(1): 85-92, Marzo 2024.
Article
in Es
| LILACS, UNISALUD, BINACIS
| ID: biblio-1551285
Responsible library:
AR41.1
RESUMEN
El sarcoma folicular de células dendríticas (SFCD) es una neoplasia maligna rara derivada de las células dendríticas foliculares. Ha sido clasificado, dadas sus características inmunohistoquímicas, como parte del grupo de los sarcomas, donde representa un porcentaje menor al 1%. Actualmente, existen menos de 1.000 reportes en la literatura a nivel mundial, lo cual plantea una dificultad no sólo diagnóstica, siendo confundido frecuentemente con neoplasias de tipo linfoide; sino también terapéutica al no existir un claro consenso sobre su manejo definitivo. Esta revisión de caso clínico describe el primer caso reportado de SFCD en Costa Rica.
ABSTRACT
Follicular dendritic cell sarcoma (SFCD) is a rare malignant neoplasm derived from follicular dendritic cells, which has been classified, given its immunohistochemical characteristics, as part of the group of sarcomas, where it represents less than 1%. Currently, there are less than 1000 reports in the literature worldwide, which generates a difficulty not only in diagnosis, being frequently confused with lymphoid type neoplasms; but also, as therapeutic as there is no clear consensus on its definitive management. This clinical case review describes the first reported case of SFCD in Costa Rica.
Key words
Full text:
1
Collection:
01-internacional
Database:
BINACIS
/
LILACS
/
UNISALUD
Main subject:
Asthma
/
Cough
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Dendritic Cell Sarcoma, Follicular
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Mediastinal Neoplasms
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Obesity
Limits:
Adult
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Female
/
Humans
Country/Region as subject:
America central
/
Costa rica
Language:
Es
Journal:
Respirar (Ciudad Autón. B. Aires)
Journal subject:
Farmacologia
/
Teraputica
/
Toxicologia
/
T¢rax
Year:
2024
Document type:
Article
Affiliation country:
Country of publication: